SR76

Batten Disease (IB3)

Male

Male

SR76

Batten Disease (IB3)

Male

Male


Please Login or Register to download images or create a PowerPoint slideshow.


Visit at age: 5 years

Fundus Photography - Right - 20/125 sc

Exemplar

Fundus Photography - Left - 20/200 sc

Exemplar

Visit at age: 5 years (Visit 2)

Goldmann Visual Field - Right - 20/125 sc

Exemplar

Goldmann Visual Field - Left - 20/160 sc

Exemplar

Visit at age: 6 years

Goldmann Visual Field - Right - Count Fingers 1' sc

Exemplar

Goldmann Visual Field - Left - Count Fingers 1' sc

Exemplar

Visit at age: 7 years

Fundus Photography - Right - 20/1250 sc

Exemplar

Fundus Photography - Left - <20/3200 sc

Exemplar

Fundus Montage - Right - 20/1250 sc

Exemplar

Fundus Montage - Left - <20/3200 sc

Exemplar

Visit at age: 9 years

Fundus Photography - Right - 20/3200 sc

Exemplar

Fundus Photography - Left - Light Perception

Exemplar

Optical Coherence Tomography - Right - 20/3200 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/3200 sc

Exemplar

Infrared Fundus Photograph - Left - Light Perception

Exemplar

Visit at age: 10 years

Optical Coherence Tomography - Right - 20/4000 sc

Exemplar

Optical Coherence Tomography - Left - Light Perception

Exemplar

Infrared Fundus Photograph - Right - 20/4000 sc

Exemplar

Infrared Fundus Photograph - Left - Light Perception

Exemplar

Visit at age: 11 years

Optical Coherence Tomography - Right - 20/4000 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/4000 sc

Exemplar

Infrared Fundus Photograph - Left - Light Perception

Exemplar

Visit at age: 12 years

Optical Coherence Tomography - Right - Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - No Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - Light Perception

Exemplar

Infrared Fundus Photograph - Left - No Light Perception

Exemplar

Visit at age: 13 years

Optical Coherence Tomography - Right - No Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - No Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - No Light Perception

Exemplar

Infrared Fundus Photograph - Left - No Light Perception

Exemplar

Case Level Images


Please Login or Register to download images or create a PowerPoint slideshow.