SR1931

Best Disease (IIB)

Male

Male

SR1931

Best Disease (IIB)

Male

Male


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Visit at age: 8 years

Fundus Photography - Right - 20/20 sc

Exemplar

Fundus Photography - Left - 20/25 -2 sc

Exemplar

Visit at age: 9 years

Fundus Photography - Right - 20/25 +2 sc

Exemplar

Fundus Photography - Left - 20/25 sc

Exemplar

Visit at age: 14 years

Fundus Photography - Right - 20/20 sc

Exemplar

Fundus Photography - Left - Count Fingers 6" sc

Exemplar

Visit at age: 16 years

Fundus Photography - Right - 20/25 -3 sc

Exemplar

Fundus Photography - Left - 20/160 sc

Exemplar

Fluorescein Angiography - Right - 20/25 -3 sc

Exemplar

Fluorescein Angiography - Left - 20/160 sc

Exemplar

Visit at age: 17 years

Optical Coherence Tomography - Right - 20/20 sc

Exemplar / OCT Stack

Optical Coherence Tomography - Left - 20/100 -1 sc

Exemplar / OCT Stack

Infrared Fundus Photograph - Right - 20/20 sc

Exemplar

Infrared Fundus Photograph - Left - 20/100 -1 sc

Exemplar

Visit at age: 18 years

Fundus Photography - Right - 20/20 +2 sc

Exemplar

Fundus Photography - Left - 20/125 sc

Exemplar

Optical Coherence Tomography - Right - 20/20 +2 sc

Exemplar / OCT Stack

Optical Coherence Tomography - Left - 20/125 sc

Exemplar / OCT Stack

Infrared Fundus Photograph - Right - 20/20 +2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/125 sc

Exemplar

Visit at age: 20 years

Optical Coherence Tomography - Right - 20/20 +1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/125 -1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 +1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/125 -1 sc

Exemplar

Visit at age: 21 years

Optical Coherence Tomography - Right - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/100 -1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/100 -1 sc

Exemplar

Visit at age: 22 years

Optical Coherence Tomography - Right - 20/25 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/80 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/25 sc

Exemplar

Infrared Fundus Photograph - Left - 20/80 sc

Exemplar

Visit at age: 23 years

Fundus Photography - Right - 20/25 -3 sc

Exemplar

Fundus Photography - Left - 20/60 -1 sc

Exemplar

Optical Coherence Tomography - Right - 20/25 -3 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/60 -1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/25 -3 sc

Exemplar

Infrared Fundus Photograph - Left - 20/60 -1 sc

Exemplar

Visit at age: 24 years

Optical Coherence Tomography - Right - 20/20 -2 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/60 -2 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/60 -2 sc

Exemplar

Visit at age: 24 years (Visit 2)

Optical Coherence Tomography - Right - 20/20 -3 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/80 +2 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -3 sc

Exemplar

Infrared Fundus Photograph - Left - 20/80 +2 sc

Exemplar

Visit at age: 24 years (Visit 3)

Optical Coherence Tomography - Right - 20/20 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/60 +1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/60 +1 sc

Exemplar

Visit at age: 25 years

Optical Coherence Tomography - Right - 20/20 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/70 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/70 sc

Exemplar

Visit at age: 26 years

Optical Coherence Tomography - Right - 20/25 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/60 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/25 sc

Exemplar

Infrared Fundus Photograph - Left - 20/60 -2 sc

Exemplar

Blue Autofluorescence - Right - 20/25 sc

Exemplar

Blue Autofluorescence - Left - 20/60 -2 sc

Exemplar

Swept-Source OCT - Right - 20/25 sc

Exemplar

Swept-Source OCT - Left - 20/60 -2 sc

Exemplar

Visit at age: 27 years

Optical Coherence Tomography - Right - 20/25 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/70 -1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/25 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/70 -1 sc

Exemplar

Blue Autofluorescence - Right - 20/25 -2 sc

Exemplar

Blue Autofluorescence - Left - 20/70 -1 sc

Exemplar

Swept-Source OCT - Right - 20/25 -2 sc

Exemplar

Swept-Source OCT - Left - 20/70 -1 sc

Exemplar

Visit at age: 28 years

Fundus Photography - Right - 20/40 sc

Exemplar

Fundus Photography - Left - 20/60 -1 sc

Exemplar

Optical Coherence Tomography - Right - 20/40 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/60 -1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/40 sc

Exemplar

Infrared Fundus Photograph - Left - 20/60 -1 sc

Exemplar

Visit at age: 28 years (Visit 2)

Optical Coherence Tomography - Right - 20/30 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/60 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/30 sc

Exemplar

Infrared Fundus Photograph - Left - 20/60 -2 sc

Exemplar

Visit at age: 29 years

Optical Coherence Tomography - Right - 20/40 +1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/125 +2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/40 +1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/125 +2 sc

Exemplar

Swept-Source OCT - Right - 20/40 +1 sc

Exemplar

Swept-Source OCT - Left - 20/125 +2 sc

Exemplar

Visit at age: 30 years

Optical Coherence Tomography - Right - 20/40 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/70 +2 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/40 sc

Exemplar

Infrared Fundus Photograph - Left - 20/70 +2 sc

Exemplar

Visit at age: 30 years (Visit 2)

Optical Coherence Tomography - Right - 20/40 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/70 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/40 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/70 sc

Exemplar

Visit at age: 31 years

Optical Coherence Tomography - Right - 20/40 +1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/70 +1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/40 +1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/70 +1 sc

Exemplar

Case Level Images


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