SR2389

Batten Disease (IB3)

Male

Male

SR2389

Batten Disease (IB3)

Male

Male


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Visit at age: 7 years

Fundus Photography - Right - 20/100 -1 sc

Exemplar

Fundus Photography - Left - 20/100 -2 sc

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Goldmann Visual Field - Right - 20/100 -1 sc

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Goldmann Visual Field - Left - 20/100 -2 sc

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Optical Coherence Tomography - Right - 20/100 -1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/100 -2 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/100 -1 sc

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Infrared Fundus Photograph - Left - 20/100 -2 sc

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Blue Autofluorescence - Right - 20/100 -1 sc

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Blue Autofluorescence - Left - 20/100 -2 sc

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Visit at age: 8 years

Fundus Photography - Right - 20/125 +1 sc

Exemplar

Fundus Photography - Left - 20/125 -1 sc

Exemplar

Goldmann Visual Field - Right - 20/125 +1 sc

Exemplar

Goldmann Visual Field - Left - 20/125 -1 sc

Exemplar

Optical Coherence Tomography - Right - 20/125 +1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/125 -1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/125 +1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/125 -1 sc

Exemplar

Visit at age: 8 years (Visit 2)

Goldmann Visual Field - Right - 20/200 +2

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Goldmann Visual Field - Left - 20/200 +2

Exemplar

Optical Coherence Tomography - Right - 20/200 +2

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/200 +2

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/200 +2

Exemplar

Infrared Fundus Photograph - Left - 20/200 +2

Exemplar

Visit at age: 9 years

Fundus Photography - Right - 10/200 sc

Exemplar

Fundus Photography - Left - 10/200 sc

Exemplar

Optical Coherence Tomography - Right - 10/200 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/200 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 10/200 sc

Exemplar

Infrared Fundus Photograph - Left - 10/200 sc

Exemplar

Visit at age: 9 years (Visit 2)

Goldmann Visual Field - Right - 10/200 -2 sc

Exemplar

Goldmann Visual Field - Left - 10/200 sc

Exemplar

Optical Coherence Tomography - Right - 10/200 -2 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/200 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 10/200 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 10/200 sc

Exemplar

Visit at age: 10 years

Goldmann Visual Field - Right - 10/300 sc

Exemplar

Goldmann Visual Field - Left - 10/300 sc

Exemplar

Optical Coherence Tomography - Right - 10/300 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/300 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 10/300 sc

Exemplar

Infrared Fundus Photograph - Left - 10/300 sc

Exemplar

Visit at age: 10 years (Visit 2)

Fundus Photography - Right - 10/300 sc

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Fundus Photography - Left - 10/300 sc

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Fundus Montage - Right - 10/300 sc

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Fundus Montage - Left - 10/300 sc

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Goldmann Visual Field - Right - 10/300 sc

Exemplar

Goldmann Visual Field - Left - 10/300 sc

Exemplar

Optical Coherence Tomography - Right - 10/300 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/300 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 10/300 sc

Exemplar

Infrared Fundus Photograph - Left - 10/300 sc

Exemplar

Case Level Images


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