SR1008

Usher Syndrome (IB1)

Female

Female

SR1008

Usher Syndrome (IB1)

Female

Female


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Visit at age: 38 years

Fundus Photography - Right - 20/200 +2

Exemplar

Fundus Photography - Left - 10/225

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Fundus Montage - Right - 20/200 +2

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Fundus Montage - Left - 10/225

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Goldmann Visual Field - Right - 20/200 +2

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Goldmann Visual Field - Left - 10/225

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Optical Coherence Tomography - Right - 20/200 +2

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/225

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/200 +2

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Infrared Fundus Photograph - Left - 10/225

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B-Scan Ultrasonography - Right - 20/200 +2

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B-Scan Ultrasonography - Left - 10/225

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Visit at age: 38 years (Visit 2)

Goldmann Visual Field - Right - 10/100 -2

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Goldmann Visual Field - Left - 10/160 -2

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Optical Coherence Tomography - Right - 10/100 -2

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/160 -2

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 10/100 -2

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Infrared Fundus Photograph - Left - 10/160 -2

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Visit at age: 39 years

Goldmann Visual Field - Right - 10/180 sc

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Goldmann Visual Field - Left - 5/300 sc

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Optical Coherence Tomography - Right - 10/180 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 5/300 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 10/180 sc

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Infrared Fundus Photograph - Left - 5/300 sc

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Visit at age: 41 years

Goldmann Visual Field - Right - 10/80 sc

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Goldmann Visual Field - Left - 10/160 -1

Exemplar

Optical Coherence Tomography - Right - 10/80 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/160 -1

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 10/80 sc

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Infrared Fundus Photograph - Left - 10/160 -1

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Blue Autofluorescence - Right - 10/80 sc

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Blue Autofluorescence - Left - 10/160 -1

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Visit at age: 42 years

Goldmann Visual Field - Right - 10/160 +1 sc

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Goldmann Visual Field - Left - 10/200 -1 sc

Exemplar

Optical Coherence Tomography - Right - 10/160 +1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/200 -1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 10/160 +1 sc

Exemplar

Infrared Fundus Photograph - Left - 10/200 -1 sc

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Visit at age: 45 years

Goldmann Visual Field - Right - 10/300 sc

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Goldmann Visual Field - Left - 10/400 sc

Exemplar

Optical Coherence Tomography - Right - 10/300 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/400 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 10/300 sc

Exemplar

Infrared Fundus Photograph - Left - 10/400 sc

Exemplar

Case Level Images


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