SR77

Best Disease (IIB)

Male

Male

SR77

Best Disease (IIB)

Male

Male


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Visit at age: 14 years

Fundus Photography - Right - 20/160 +1 sc

Exemplar

Fundus Photography - Left - 20/16 -1 sc

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Optical Coherence Tomography - Right - 20/160 +1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/16 -1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/160 +1 sc

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Infrared Fundus Photograph - Left - 20/16 -1 sc

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Fluorescein Angiography - Right - 20/160 +1 sc

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Fluorescein Angiography - Left - 20/16 -1 sc

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Visit at age: 14 years (Visit 2)

Fundus Photography - Right - 20/80 -1 sc

Exemplar

Optical Coherence Tomography - Right - 20/80 -1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/80 -1 sc

Exemplar

Visit at age: 14 years (Visit 3)

Fundus Photography - Right - 20/70 +1 sc

Exemplar

Optical Coherence Tomography - Right - 20/70 +1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/70 +1 sc

Exemplar

Visit at age: 14 years (Visit 4)

Fundus Photography - Right - 20/125 sc

Exemplar

Optical Coherence Tomography - Right - 20/125 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/15 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/125 sc

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Infrared Fundus Photograph - Left - 20/15 -2 sc

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Visit at age: 14 years (Visit 5)

Fundus Photography - Right - 20/70 -1 sc

Exemplar

Fundus Photography - Left - 20/20 sc

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Optical Coherence Tomography - Right - 20/70 -1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/70 -1 sc

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Infrared Fundus Photograph - Left - 20/20 sc

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Visit at age: 15 years

Fundus Photography - Right - 20/20 -2

Exemplar

Optical Coherence Tomography - Right - 20/20 -2

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -2

Exemplar

Visit at age: 15 years (Visit 2)

Optical Coherence Tomography - Right - 20/20 +1

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 +1

Exemplar

Visit at age: 15 years (Visit 3)

Optical Coherence Tomography - Right - 20/15 -3

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/15 -3

Exemplar

Visit at age: 15 years (Visit 4)

Optical Coherence Tomography - Right - 20/15 -3

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/15 -3

Exemplar

Visit at age: 15 years (Visit 5)

Fundus Photography - Right - 20/20 +2

Exemplar

Optical Coherence Tomography - Right - 20/20 +2

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 +2

Exemplar

Visit at age: 15 years (Visit 6)

Optical Coherence Tomography - Right - 20/20

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20

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Infrared Fundus Photograph - Left - 20/20 -1 sc

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Visit at age: 16 years

Fundus Photography - Right - 20/50 -2 sc

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Fundus Photography - Left - 20/70 sc

Exemplar

Optical Coherence Tomography - Right - 20/50 -2 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/70 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/50 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/70 sc

Exemplar

Visit at age: 16 years (Visit 2)

Optical Coherence Tomography - Right - 20/25 +2 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 -3 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/25 +2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 -3 sc

Exemplar

Visit at age: 16 years (Visit 3)

Optical Coherence Tomography - Right - 20/20 -3 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/15 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -3 sc

Exemplar

Infrared Fundus Photograph - Left - 20/15 sc

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Visit at age: 16 years (Visit 4)

Optical Coherence Tomography - Right - 20/25 -1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/15 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/25 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/15 sc

Exemplar

Visit at age: 17 years

Optical Coherence Tomography - Right - 20/20 -3 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/15 -3 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -3 sc

Exemplar

Infrared Fundus Photograph - Left - 20/15 -3 sc

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Visit at age: 17 years (Visit 2)

Optical Coherence Tomography - Right - 20/20 -3 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -3 sc

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Infrared Fundus Photograph - Left - 20/20 sc

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Visit at age: 17 years (Visit 3)

Fundus Photography - Right - 20/30 -2 sc

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Fundus Photography - Left - 20/20 sc

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Optical Coherence Tomography - Right - 20/30 -2 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/30 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 sc

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Visit at age: 20 years

Fundus Photography - Right - 20/30 -2 sc

Exemplar

Fundus Photography - Left - 20/20 -2 sc

Exemplar

Optical Coherence Tomography - Right - 20/30 -2 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 -2 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/30 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 -2 sc

Exemplar

Visit at age: 20 years (Visit 2)

Optical Coherence Tomography - Right - 20/30 -1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/30 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 -1 sc

Exemplar

Visit at age: 20 years (Visit 3)

Optical Coherence Tomography - Right - 20/25 -2 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/25 -2 sc

Exemplar

Visit at age: 20 years (Visit 4)

Optical Coherence Tomography - Right - 20/40 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/40 sc

Exemplar

Visit at age: 20 years (Visit 5)

Fundus Photography - Right - 20/40 -2 sc

Exemplar

Fundus Photography - Left - 20/20 sc

Exemplar

Optical Coherence Tomography - Right - 20/40 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/40 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 sc

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Blue Autofluorescence - Right - 20/40 -2 sc

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Blue Autofluorescence - Left - 20/20 sc

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Visit at age: 20 years (Visit 6)

Optical Coherence Tomography - Right - 20/25 -2 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/25 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 sc

Exemplar

Visit at age: 20 years (Visit 7)

Fundus Photography - Right - 20/40 -1 sc

Exemplar

Fundus Photography - Left - 20/20 sc

Exemplar

Optical Coherence Tomography - Right - 20/40 -1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/40 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 sc

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Fluorescein Angiography - Left - 20/20 sc

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Visit at age: 22 years

Fundus Photography - Right - 20/20 -3 sc

Exemplar

Fundus Photography - Left - 20/25 sc

Exemplar

Optical Coherence Tomography - Right - 20/20 -3 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/25 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -3 sc

Exemplar

Infrared Fundus Photograph - Left - 20/25 sc

Exemplar

Visit at age: 22 years (Visit 2)

Optical Coherence Tomography - Right - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/15 -2 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/15 -2 sc

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Visit at age: 23 years

Fundus Photography - Right - 20/20 -1 sc

Exemplar

Fundus Photography - Left - 20/20 -1 sc

Exemplar

Optical Coherence Tomography - Right - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 -1 sc

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Blue Autofluorescence - Right - 20/20 -1 sc

Exemplar

Blue Autofluorescence - Left - 20/20 -1 sc

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Visit at age: 24 years

Fundus Photography - Right - 20/20 sc

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Fundus Photography - Left - 20/20 sc

Exemplar

Optical Coherence Tomography - Right - 20/20 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 sc

Exemplar

Visit at age: 24 years (Visit 2)

Optical Coherence Tomography - Right - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 sc

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Visit at age: 25 years

Optical Coherence Tomography - Right - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/20 -2 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/20 -2 sc

Exemplar

Visit at age: 25 years (Visit 2)

Fundus Photography - Right - 20/20 -1 sc

Exemplar

Fundus Photography - Left - 20/70 -1 sc

Exemplar

Optical Coherence Tomography - Right - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/70 -1 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/70 -1 sc

Exemplar

Visit at age: 25 years (Visit 3)

Optical Coherence Tomography - Right - 20/20 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/60 -2 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -2 sc

Exemplar

Infrared Fundus Photograph - Left - 20/60 -2 sc

Exemplar

Visit at age: 25 years (Visit 4)

Optical Coherence Tomography - Right - 20/20 -1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/60 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 -1 sc

Exemplar

Infrared Fundus Photograph - Left - 20/60 sc

Exemplar

Visit at age: 25 years (Visit 5)

Optical Coherence Tomography - Right - 20/20 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/60 -1 sc

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20 sc

Exemplar

Infrared Fundus Photograph - Left - 20/60 -1 sc

Exemplar

Visit at age: 25 years (Visit 6)

Optical Coherence Tomography - Right - 20/20

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 20/50

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/20

Exemplar

Infrared Fundus Photograph - Left - 20/50

Exemplar

Case Level Images


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