SR74

Batten Disease (IB3)

Male

Male

SR74

Batten Disease (IB3)

Male

Male


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Visit at age: 7 years

Fundus Photography - Right - 20/200 sc

Exemplar

Fundus Photography - Left - 10/160 sc

Exemplar

Optical Coherence Tomography - Right - 20/200 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 10/160 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - 20/200 sc

Exemplar

Infrared Fundus Photograph - Left - 10/160 sc

Exemplar

Visit at age: 7 years (Visit 2)

Optical Coherence Tomography - Right - <1/700 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - 3/200 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - <1/700 sc

Exemplar

Infrared Fundus Photograph - Left - 3/200 sc

Exemplar

Visit at age: 8 years

Optical Coherence Tomography - Right - <1/700 sc

Exemplar / OCT Stack
OCT Stack

Optical Coherence Tomography - Left - <1/700 sc

Exemplar / OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - <1/700 sc

Exemplar

Infrared Fundus Photograph - Left - <1/700 sc

Exemplar

Visit at age: 9 years

Optical Coherence Tomography - Right - No Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - No Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - No Light Perception

Exemplar

Infrared Fundus Photograph - Left - No Light Perception

Exemplar

Visit at age: 11 years

Optical Coherence Tomography - Right - No Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack

Optical Coherence Tomography - Left - No Light Perception

Exemplar / OCT Stack
OCT Stack
OCT Stack
OCT Stack

Infrared Fundus Photograph - Right - No Light Perception

Exemplar

Infrared Fundus Photograph - Left - No Light Perception

Exemplar

Case Level Images


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